Urticaria pigmentosa: A rare case report

• Author Details:   
• Krishnendra Varma
• Noreen Munshi ^*
• Ujjwal Kumar Kumar

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Mastocytosis is a rare, acquired multisystem disorder of increased number of mast cell in the skin and other tissues. Mastocytosis is caused by several activating mutations in the KIT gene.¹ Although mastocytosis is primarily a systemic disorder, it often presents with skin lesions to dermatologists. Urticaria Pigmentosa is the most common pattern of cutaneous mastocytosis in adults and children.

Keywords: Urticaria Pigmentosa, Mastocytosis.